Idiopathic dilatation of the right atrium. REPORT OF FOUR FETAL CASES

Idiopathic dilatation of the right atrium (IDRA) is a rare anomaly defined as an isolated enlargement of the right atrium (RA) in the absence of other cardiac lesions or a condition cause RA dilatation. The clinical presentation ranging from asymptomatic to cardiac failure or even sudden death. It can be associated with atrial arrhythmias, thrombus formation and congestive heart failure. Antiplatelet prophylaxis is carried out in most described cases due to the risk of pulmonary thrombosis (and systemic if SIAD is present). The main indications for surgical reduction are rapid progression of growth, compression of adjacent structures and refractory arrhythmias. We report 4 cases of IDRA observed during prenatal diagnosis and describe the intrauterine and the postnatal course and management.